Gorham's Syndrome Associated with Chiari I Malformation and Recurrent Meningitis without Fistula: Case Report
Published: May 1, 2018 | DOI: https://doi.org/10.7860/JCDR/2018/35304.11565
Fernando Antônio Oliveira Costa, Othello Moreira Fabião Neto, Frederico Lima Gibbon, Guilherme Gago Silva, Luciana Azambuja AL Alam
1. MD, PhD, Department of Neurosurgery, Universidade Católica de Pelotas, Pelotas, Rio Grande do Sul, Brazil.
2. MD, MSc, Department of Neurosurgery, Universidade Católica de Pelotas, Pelotas, Rio Grande do Sul, Brazil.
3. Medical Student, Department of Neurosurgery, Universidade Católica de Pelotas, Pelotas, Rio Grande do Sul, Brazil.
4. Medical Student, Department of Neurosurgery, Universidade Católica de Pelotas, Pelotas, Rio Grande do Sul, Brazil.
5. Medical Student, Department of Neurosurgery, Universidade Católica de Pelotas, Pelotas, Rio Grande do Sul, Brazil.
Correspondence
Frederico Lima Gibbon,
Av. Major Carlos Pinto 123, Casa 14, Rio Grande, Rio Grande do Sul, Brazil.
E-mail: fredericogibbon@gmail.com
Gorham’s syndrome is a rare osteolytic disease in which progressive and spontaneous resorption of bone occurs. We present a case of a boy who presented with Chiari I malformation and recurrent meningitis without fistula. The patient was submitted to occipital bone biopsy and due to lymphocytic infiltration and intraosseous vascular ectasia the diagnosis of Gorham-Stout Syndrome was made. The patient underwent conservative treatment but, unfortunately he died by cardiorespiratory arrest secondary to atlanto-occipital dislocation. This case emphasizes the rarity of this pathology and the previously unreported association with recurrent meningitis without fistula.
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